台北榮總內科總查房與臨床病理討論會

Motility Disorders of The Esophagus

許文虎醫師
台北榮民總醫院胸腔外科

June 12, 1996




INTRODUCTION

Clinically, some patients suffered from heartburn, regurgitation, dysphagia, bleeding or chest pain. The motility disorders of esophagus frequently were the cause of the symptoms. In order to solve the problems, a clear understanding of pathophysiologic mechanism of swallowing and determination of the precise functional abnormality of symptoms are essential for the choice of treatment.

PHYSIOLOGY OF DEGLUTITION

The human esophagus is a muscular tube whose major function is transport of food from the mouth to the stomach. It is founded by a tonically contracted circular muscle sphincter at each end. The upper esophageal sphincter (UES) and the proximal esophagus belong to striated muscle portion, while the distal esophagus belongs to smooth muscle portion. The striated muscle in the proximal esophagus receives direct input to motor end plates and that the cell bodies are located in nucleus ambiguous (NA). In contrast, the smooth muscle portion, like that of the rest of the gastrointestinal tract, has indirect neural input into the muscles through the myenteric plexus. The ganglia originate in the dorsal motor nucleus (DMN) of the vagus nerve.

The traditionally swallowing or deglutition has been divided into three stages in the oral (voluntary) stage, the pharyngeal (involuntary) stage, and the esophageal stage. These three are closely coordinated and continuing processes that are regulated through the swallowing center in the medulla. The normal subjects have the good relaxation of UES and LES and good esophageal peristalsis. But some of the abnormal contractions such as non-peristaltic contraction, simultaneous contraction, nontransmitted contraction, retrograde contraction, will be found in esophageal motility disorder patients.

METHODOLOGY FOR ASSESSING MOTOR DYSFUNCTION :

The specific methods for assessing motor dysfunction of the esophagus and pharyngoesophageal function are :

  1. Videotape contrast radiography
  2. Manometry
  3. Transit scintigraphy
  4. Manofluorography

The manometry is used most commonly. The provocative esophageal function test, such as acid perfusion test and edrophonium test, has greatest role in differentiating esophageal from cardiac pain.

SYMPTOMS OF MOTILITY DISORDERS OF ESOPHAGUS
The main symptoms of esophageal motility disorders are :
  1. Dysphagia
  2. Chest pain, heartburn
  3. Regurgitation
  4. Bleeding
DISEASES OF THE ESOPHAGEAL MOTILITY DISORDERS :

According to the type of esophageal muscles involved, we divided the diseases with esophageal motor disorders into two groups :

  1. Diseases involving the pharyngo esophageal junction and the proximal esophagus -- striated (Skeletal) muscle :
    They usually cause the cricopharyngeal dysphagia and may be classified into 4 categories :
    1. Neurogenic
      CVA
      Amyotrophic lateral sclerosis
      Bulbar poliomyelitis
      Riley-Day syndrome
      Multiple sclerosis
      Parkinson's disease
    2. Myogenic :
      Myasthenia gravis
      Muscular dystrophy
      Dermatomyositis
      Polymyositis
      Thyrotoxicosis
    3. Structural
      Cricopharyngeal diverticulum
      Cricopharyngeal dysfunction
      Postoro laryngeal surgery
      Postirradiation
      Caustic burn
    4. Psychiatric
      Globus hystericus (?)
  2. Diseases involving the body of the esophagus and the lower esophageal sphincter -- smooth muscle
    The disorders involving esophageal smooth muscle are :
    1. Primary dysmotlities
      Achalasia
      Diffuse esophageal spasm
      Nutcracker esophagus
      Hypertensive LES
      Nonspecific motility dysfunction
    2. Secondary dysmotilities : Progressive systemic sclerosis - scleroderma
      Multiple sclerosis
      Diabetic neuropathy
      Chaga's disease
      Reflux esophagitis
      Parkinsonism
      Alcoholism
      Thyrotoxicosis
      Amyloidosis
    3. Congenital
      Riley-Day syndrome
MANOMETRIC CHARACTERISTICS :
  1. Disorder of UES
    The disorder of UES may be due to any or combination of the followings :
    1. Hypertensive UES
    2. Hypotensive UES
    3. Abnormalities of UES relaxation
      1. Incomplete relaxation
      2. Delayed relaxation
      3. Premature closure
  2. Primary esophageal motility disorders :
    PRIMARY ESOPH. MOTILITY DISORDERS MANOMETRIC CRITERIA
    *Achalasia Absent peristalsis-simultaneous
     Incomplete relaxation of LES
     Hypertensive LES
     Increased IEP
    *Diffuse esoph. spasm (DES) Normal peristalsis with nonpropulsive
     high amplitude wave
    *Nutcracker esophagus Peristalsis with high amplitude
      (>180 mmHg)
    Prolong duration (>6.0s)
    *Hypertensive LES LESP > 45 mmHg
    Abnormal LES relaxation
    *Nonspecific esoph. motility disorders increased nontransmitted contraction
    (NEMD)  (>20% of ws.)
    Tripple-peaked contraction
    Retrograde contraction
    Low amplitude contraction (<30 mmHg)
    Isolated, incomplete LES relaxation
    prolong duration peristaltic waves (>6s)

  3. Secondary esophageal motility disorders : The secondary esophageal motility disorders may be divided into the following categories of disease origin :
    1. Collagen-Vascular diseases
    2. Endocrine and metabolic disease
    3. Neuromuscular disease
    4. Chronic idiopathic intestinal pseudoobstruction
    5. Chaga's disease
    6. Aging
    Every category of the diseases involved the different portion of the esophagus and had it specific or nonspecific patterns in manometric study.
RADIOLOGY

The esophagogram or UGI series is frequently used in radiology for motor disorders of esophagus. In esophagogram, achalasia had characteristics of 'Bird Beak' configuration and may divide into 3 stages,

Stage I -- minimal -- esophageal diameter of less than 4 cm.
Stage II -- moderate -- esophageal diameter of 4 to 6 cm.
Stage III -- severe -- esophageal diameter of more than 6 cm.

Most patients with vigorous achalasia have stage I disease. In diffuse esophageal spasm the esophagogram may have curling or corkscrew shape or appearance of pseudo- diverticulosis.

The motor disorder due to gastroesophageal reflux may have esophageal hiatal hernia and esophagitis in UGI series examination. For the Zenker's diverticulum or epiphrenic diverticulum, esophagogram will demonstrate a protruding barium shadow outside the esophageal wall.

NON-CARDIAC CHEST PAIN : TREATMENT :

For secondary esophageal motility disorders the treatment should be conservatively and medically to relieve the symptom at the beginning. For the primary esophageal motility disorders the possible therapies were as the following table :

POSSIBLE THERAPIES FOR PRIMARY ESOPH. MOTILITY DISORDERS
I. Medical :
  1. Nitrates : Nitroglycerin, isorbide
  2. Anticholinergics : Dicyclomine
  3. Psychotropic drugs : Diazepam
  4. Calcium blocker : Nifedipine
  5. Smooth m. relaxant : Hydralazine
  6. Static dilatation : 50 French
  7. Pneumatic dilatation
II. Surgical :
  Esophagomyotomy
  If surgery was selected, the operative procedures will be performed for specific location of disease. The procedures and operative results will be summarized in the following table

SURGERY FOR ESOPHAGEAL MOTILITY DISORDERS

Motility Disorders   Surgery  Result Satisfied
I. Pharyngoesophageal Dysfunction  Cricopharyngeal myotomy
  CVA  "  64%
  Zenker's diverticulum  "(diverticulopexy or
 diverticulectomy)   84%
II. Motor Disorders of Esoph. Body:  Long Esophageal Myotomy
  DES  "  40~100%
  Vigorous achalasia  " (anti-reflux op)  86%
  NEMD with diverticulum  " (diverticulopexy or
  diverticulectomy)
III. LES Dysfunction  Modified Heller's Myotomy
  Achalasia  " (anti-reflux op)  90%
IV. LES Incompetency :  Anti-reflux op
  GER with complications  "  92%
V. End Stage Motility Disorders  Esophageal Resection and
   of Esoph.  interposition with stomach or  90%
 colon or jejunum


CONCLUSION :

The GER or with hiatal hernia, achalasia, DES, nutcracker esophagus, and hypertensive LES are the common primary motility disorders of the esophagus. All of them have manometric characteristics and can be treated medically and surgically. Different surgeries are recommended after failure of medical treatment. Surgeries will be esophagomyotomy for cricopharyngeal dysfunction, excision or with myotomy for diverticulum, long esophagomyotomy for DES or nutcracker esophagus or hypertensive LES, modified Heller's myotomy for achalasia, anti-reflux operation for GER and scleroderma. Some surgical experiences for treatment of motor disorders of esophagus in Division of Thoracic Surgery of Taipei VGH will be presented and discussed.



REFERENCES:

  1. Tom R DeMeester, Hubert J Stein, Surgery for esophageal motor disorders. Donald 0 Castell ed. The Esophagus Little, Brown and Company 1992, 401-39.
  2. Earle W, Wilkins Jr. Motor disturbances of deglutition Thomas W Shields ed General Thoracic Surgery, 4th edition. A Waverly Company. 1994, 1541-53.
  3. Christine Boag Dalton PA, Donald O. Castell. Esophageal motility disorders. David W. Gelfand, Joel E. Richter eds. Dysphagia, diagnosis and treatment. igaku-Shoin Company. 1989, 257-79.
  4. Castell, Esophageal Motility Testing, second edition 1994, Appleton and Lange.


回到頁首 榮總首頁 本科首頁 回上一頁