Congenital hemihypertrophy associated with hepatoblastoma - report of two patients
台中榮民總醫院 外科部 小兒外科
周佳滿 陳厚全 張振昌

Hemihypertrophy clinically manifestates asymmetric growth of carnium, face, trunk, limbs, with or without visceral involvement. It could be an isolated finding in an normal individual or occur in several syndromes such as Beckwith-Wiedemann syndrome. Hemihypertrophy usually occurs sporadically and 1:86,000 in incidence. The clinical feature of hemihypertrophy is associated with neoplasm, most frequently with Wilms tumor, adrenocortical carcinoma, hepatoblastoma and rarely with rhabdomyosarcoma, neuroblastoma, pheochromocytoma or undifferentiated sarcoma of lung. The overall incidence of abdominal neoplasm associated with hemihypertrophy is 5.9% and average annual incidence in the first 4 years of life is 0.027 per person-year. In this article, we describe 2 patients with congenital asymmetry of limbs who presented with hepatoblastoma and were underwent surgical intervention. The postoperative recovery were smooth and the patients were doing well at present follow up.